- Poland Syndrome:
- Is a rare chest wall deformity consisting of:
- Unilateral chest wall hypoplasia and unilateral upper limb deformity
- There can be:
- Absence or hypoplasia of the breast
- Absent pectoralis major or minor
- Absent nipple
- Absent costal cartilages
- Rib abnormalities
- Upper limb deformities including:
- Syndactyly
- Micromelia
- Brachydactyly
- This rare disease affects men three times more commonly than women
- Poland syndrome is thought to occur due to:
- An interruption of the embryonic blood supply to the subclavian artery:
- At the 6th week of embryonic development
- An interruption of the embryonic blood supply to the subclavian artery:
- The defects can be corrected surgically:
- Repair can include:
- Reconstruction of anaplastic ribs:
- Using bone grafts or prosthetic mesh
- Muscle flaps such as latissimus dorsi flap to correct muscle hypoplasia
- Breast implants or autologous fat grafting for breast hypoplasia
- Reconstruction of anaplastic ribs:
- Repair can include:
- Is a rare chest wall deformity consisting of:
- References:
- Kulkarni D, Dixon JM. Congenital abnormalities of the breast. Women’s Health. 2012;8(1):75–88.
- Baldelli I, Santi P, Dova L, Cardoni G, Ciliberti R, Franchelli S, Merlo DF, et al. Body image disorders and surgical timing in patients affected by Poland Syndrome: data analysis of 58 case studies. Plast Reconstr Surg. 2016;137(4):1273-1282.
- Fokin AA, Robicsek F. Poland’s syndrome revisited. Ann Thorac Surg. 2002:74(6),2218–2225.
#Arrangoiz #BreastSurgeon #CancerSurgeon #SurgicalOncologist #PolandSyndrome
Rodrigo Arrangoiz MS, MD, FACS, FSSO 